Squamous Cell Carcinoma Arising from Remnant of Mullerian Duct With 47XYY Karyotype – Rare Case

Persistent Mullerian duct syndrome (PMDS) is a rare type of male pseudohermaphroditism characterized by the presence derivatives (uterus, fallopian tubes and upper vagina), cryptorchidism either unilateral or bilateral along with inguinal hernia in phenotypically genotypically person. PMDS rarely associated malignancies, most common being testicular germ cell tumours. Occasional case Adenocarcinoma arising PMD remnant structure reported.
 We report an unusual squamous carcinoma (SCC) from presented hematuria Also, this patient had karyotype 47XYY (Jacob syndrome). Both these are hitherto unreported English literature to best our knowledge.